Two-to-one AV block associated with the congenital long QT syndrome
Details
Serval ID
serval:BIB_A9C085626DCA
Type
Article: article from journal or magazin.
Publication sub-type
Case report (case report): feedback on an observation with a short commentary.
Collection
Publications
Institution
Title
Two-to-one AV block associated with the congenital long QT syndrome
Journal
Journal of Cardiovascular Electrophysiology
ISSN
1045-3873 (Print)
Publication state
Published
Issued date
01/1999
Volume
10
Number
1
Pages
108-13
Notes
Case Reports
Journal Article --- Old month value: Jan
Journal Article --- Old month value: Jan
Abstract
INTRODUCTION: Conduction abnormalities associated with long QT syndrome (LQTS) have been reported as "pseudo 2:1 AV block" due to sinus intervals shorter than ventricular refractoriness. METHOD AND RESULTS: We report the electrophysiologic characteristics of a patient suffering from congenital LQTS with episodes of true 2:1 AV block. Induction of 2:1 infra-Hisian blocks and return to 1:1 conduction were observed using single atrial and ventricular extrastimuli. The block was located in the Purkinje network but not in the myocardium. CONCLUSION: The His-Purkinje system of our LQTS patient displayed dynamic properties with a strong increase in refractoriness for short-long sequences and a decrease for long-short sequences that triggered intermittent 2:1 AV blocks.
Keywords
Adolescent
Cardiac Pacing, Artificial
*Electrocardiography
Female
Follow-Up Studies
Heart Block/*etiology/physiopathology/therapy
Humans
Long QT Syndrome/complications/*congenital/physiopathology
Purkinje Fibers/physiopathology
Sympathectomy
Pubmed
Web of science
Create date
28/01/2008 10:04
Last modification date
20/08/2019 15:13