Two-to-one AV block associated with the congenital long QT syndrome
Détails
ID Serval
serval:BIB_A9C085626DCA
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Institution
Titre
Two-to-one AV block associated with the congenital long QT syndrome
Périodique
Journal of Cardiovascular Electrophysiology
ISSN
1045-3873 (Print)
Statut éditorial
Publié
Date de publication
01/1999
Volume
10
Numéro
1
Pages
108-13
Notes
Case Reports
Journal Article --- Old month value: Jan
Journal Article --- Old month value: Jan
Résumé
INTRODUCTION: Conduction abnormalities associated with long QT syndrome (LQTS) have been reported as "pseudo 2:1 AV block" due to sinus intervals shorter than ventricular refractoriness. METHOD AND RESULTS: We report the electrophysiologic characteristics of a patient suffering from congenital LQTS with episodes of true 2:1 AV block. Induction of 2:1 infra-Hisian blocks and return to 1:1 conduction were observed using single atrial and ventricular extrastimuli. The block was located in the Purkinje network but not in the myocardium. CONCLUSION: The His-Purkinje system of our LQTS patient displayed dynamic properties with a strong increase in refractoriness for short-long sequences and a decrease for long-short sequences that triggered intermittent 2:1 AV blocks.
Mots-clé
Adolescent
Cardiac Pacing, Artificial
*Electrocardiography
Female
Follow-Up Studies
Heart Block/*etiology/physiopathology/therapy
Humans
Long QT Syndrome/complications/*congenital/physiopathology
Purkinje Fibers/physiopathology
Sympathectomy
Pubmed
Web of science
Création de la notice
28/01/2008 11:04
Dernière modification de la notice
20/08/2019 16:13