Orbital rhabdomyosarcoma: Clinicopathologic correlation, management and follow-up in two newborns. A preliminary report.

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Serval ID
serval:BIB_F68BFDF95DCD
Type
Article: article from journal or magazin.
Collection
Publications
Institution
Title
Orbital rhabdomyosarcoma: Clinicopathologic correlation, management and follow-up in two newborns. A preliminary report.
Journal
Orbit
Author(s)
Spahn B., Nenadov-Beck M.
ISSN
1744-5108[electronic]
Publication state
Published
Issued date
2001
Volume
20
Number
2
Pages
149-156
Language
english
Abstract
Rhabdomyosarcoma (RMS) is the most common primary malignant tumor of the orbit in childhood. The average age of onset is around seven years. In the present paper, the authors present the clinical and radiological findings in two newborns with histopathologically confirmed orbital rhabdomyosarcoma. A review of the literature was also carried out. In both children, the first sign leading to a visit was a unilateral proptosis, without symptoms or any other sign. Both underwent a CT-scan and an MRI. Confirmation of the histology was made by an open sky biopsy. The children were first treated by chemotherapy but had incomplete resolution of the tumor after more than 11 months for the first case and 9 months for the second. Since the parents of both children refused exenteration, radiotherapy had to be resorted to because of the incomplete response to chemotherapy. Our therapeutic approach and the outcome of these two cases are discussed.
Pubmed
Create date
28/01/2008 12:42
Last modification date
20/08/2019 16:23
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