Lupus-erythematodes-discoides-artige Dermatose bei einer Konduktorin der septischen Granulomatose. [Lupus erythematosus discoid-like dermatosis in a carrier of septic granulomatosis]

Détails

ID Serval
serval:BIB_CD90F6EEC16E
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Titre
Lupus-erythematodes-discoides-artige Dermatose bei einer Konduktorin der septischen Granulomatose. [Lupus erythematosus discoid-like dermatosis in a carrier of septic granulomatosis]
Périodique
Hautarzt
Auteur(s)
Hafner  J., Panizzon  R., Bruckner-Tuderman  L., Wuthrich  B., Seger  R. A., Burg  G.
ISSN
0017-8470 (Print)
Statut éditorial
Publié
Date de publication
07/1993
Volume
44
Numéro
7
Pages
452-6
Notes
Case Reports
English Abstract
Journal Article --- Old month value: Jul
Résumé
We present a clinically atypical case of discoid lupus erythematosus in the mother of a boy with chronic granulomatous disease. In this disorder, the phagocytes are unable to produce superoxide anion to degrade incorporated microorganisms. In addition to a discoid lupus erythematosus-like skin disease, recurrent stomatitis aphthosa, hidradenitis suppurativa and Raynaud phenomenon are markedly associated with heterozygote carriers of chronic granulomatous disease. Based on this conspicuous association, diverse models concerning the pathogenesis of lupus erythematosus are discussed.
Mots-clé
Adult Antibodies, Antinuclear/analysis Antigen-Antibody Complex/analysis Complement C1q/analysis Facial Dermatoses/genetics/pathology Female Fluorescent Antibody Technique Granulomatous Disease, Chronic/*genetics/pathology *Heterozygote Detection Humans Immunoglobulins/analysis Lupus Erythematosus, Discoid/*genetics/pathology Sex Chromosome Aberrations/*genetics Skin/pathology *X Chromosome
Pubmed
Web of science
Création de la notice
25/01/2008 16:54
Dernière modification de la notice
20/08/2019 15:48
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