Expert management of congenital portosystemic shunts and their complications.

McLin, V.A.; Franchi-Abella, S.; Brütsch, T.; Bahadori, A.; Casotti, V.; de Ville de Goyet, J.; Dumery, G.; Gonzales, E.; Guérin, F.; Hascoet, S.; Heaton, N.; Kuhlmann, B.; Lador, F.; Lambert, V.; Marra, P.; Plessier, A.; Quaglia, A.; Rougemont, A.L.; Savale, L.; Sarma, M.S.; Sitbon, O.; Superina, R.A.; Uchida, H.; van Albada, M.; Johannes van der Doef, H.P.; Vilgrain, V.; Wacker, J.; Zwaveling, N.; Debray, D.; Wildhaber, B.E.

doi:10.1016/j.jhepr.2023.100933

Expert management of congenital portosystemic shunts and their complications.

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Serval ID

serval:BIB_BC68A5AA3DC7

Type

Article: article from journal or magazin.

Collection

Publications

Institution

UNIL/CHUV

Title

Expert management of congenital portosystemic shunts and their complications.

Journal

JHEP reports

Author(s)

McLin V.A., Franchi-Abella S., Brütsch T., Bahadori A., Casotti V., de Ville de Goyet J., Dumery G., Gonzales E., Guérin F., Hascoet S., Heaton N., Kuhlmann B., Lador F., Lambert V., Marra P., Plessier A., Quaglia A., Rougemont A.L., Savale L., Sarma M.S., Sitbon O., Superina R.A., Uchida H., van Albada M., Johannes van der Doef H.P., Vilgrain V., Wacker J., Zwaveling N., Debray D., Wildhaber B.E.

ISSN

2589-5559 (Electronic)

ISSN-L

2589-5559

Publication state

Published

Issued date

01/2024

Peer-reviewed

Oui

Volume

Number

Pages

100933

Language

english

Notes

Publication types: Journal Article ; Review
Publication Status: epublish

Abstract

Congenital portosystemic shunts are often associated with systemic complications, the most challenging of which are liver nodules, pulmonary hypertension, endocrine abnormalities, and neurocognitive dysfunction. In the present paper, we offer expert clinical guidance on the management of liver nodules, pulmonary hypertension, and endocrine abnormalities, and we make recommendations regarding shunt closure and follow-up.

Keywords

adenoma, congenital portosystemic shunt, focal nodular hyperplasia, hepatocellular carcinoma, hyperandrogenism, hyperinsulinism, hypoglycemia, occlusion test, portal pressure, puberty, pulmonary hypertension, β-catenin

OAI-PMH

oai:serval.unil.ch:BIB_BC68A5AA3DC7

DOI

10.1016/j.jhepr.2023.100933

Pubmed

38234409

Web of science

001159386300001

Open Access

Yes

Create date

22/01/2024 16:02