Article: article from journal or magazin.
Case report (case report): feedback on an observation with a short commentary.
Kartagener's syndrome: clinical presentation and cardiosurgical aspects
Annals of Thoracic Surgery
Case Reports Journal Article --- Old month value: Nov
BACKGROUND: Long-term observations in patients with Kartagener's syndrome (situs inversus, bronchiectasis, and sinusitis) are rare. The role of additional cardiac malformations and their surgical repair is not well known. METHODS: Nine patients (5 female and 4 male) with Kartagener's syndrome were identified and followed. Four patients had associated cardiac anomalies; 4 underwent total surgical repair at the ages of 4 (2 patients), 7, and 34 years. RESULTS: The postoperative period was uneventful, and these 4 patients are doing well 7 months and 2, 9, and 19 years after repair. The other patients are being treated with conservative therapy and are in relatively good condition. CONCLUSIONS: This disease can be temporarily benign when treated with antibiotics and physiotherapy. Associated cardiac anomalies seem to be quite common, and such patients need careful cardiologic follow-up. Surgical intervention can be safely performed in patients suffering from Kartagener's syndrome associated with a congenital cardiac malformation and produces good long-term results. Bilateral lung transplantation seems to be the therapy of choice in patients with respiratory insufficiency but without concomitant cardiac anomalies.
Aftercare Cardiac Surgical Procedures/methods Child Child, Preschool Female Follow-Up Studies Humans Infant Infant, Newborn Kartagener Syndrome/diagnosis/genetics/*surgery Lung Transplantation Male Treatment Outcome
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