Pulmonary valve stenosis due to undifferentiated pleomorphic sarcoma

Détails

Ressource 1Télécharger: BIB_836C651E0085.P001.pdf (866.14 [Ko])
Etat: Public
Version: Final published version
ID Serval
serval:BIB_836C651E0085
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Titre
Pulmonary valve stenosis due to undifferentiated pleomorphic sarcoma
Périodique
Cardiovascular Medicine
Auteur(s)
Antiochos P., Monney P., Qanadli SD., Schlueter L., Rotman S., Descloux E., Niclauss L., Hurni M., Muller O.
Statut éditorial
Publié
Date de publication
06/2015
Volume
18
Numéro
6
Pages
186-190
Langue
anglais
Résumé
Pulmonary artery sarcomas are uncommon intracardiac tumours with poor prognosis. We report the case of a 69-year-old woman in good health presenting with rapidly progressive dyspnoea and an unfamiliar systolic murmur. Echocardiography revealed pulmonary valve stenosis due to an obstructing mobile mass. Imaging studies confirmed the presence of a contrast-enhancing lesion adherent to the valve, extending into the pulmonary trunk and right ventricular outflow tract, and suggestive of malignancy.
Endovascular biopsy was attempted with no success. Surgical resection with autologous graft valve replacement and pulmonary artery reconstruction was performed. Postoperative histological examination
confirmed the diagnosis of an undifferentiated pleomorphic sarcoma. Pulmonary artery sarcoma should be considered as a rare differential diagnosis in patients presenting with dyspnoea and a crescendo-decrescendo systolic murmur increasing with inspiration. Echocardiography is a useful first diagnostic approach but multi-imaging assessment is almost always necessary for definite diagnosis. Our case provides insights into the challenges met by cardiologists, radiologists and cardiac surgeons in the management of such cases.
Création de la notice
07/09/2015 10:58
Dernière modification de la notice
20/08/2019 15:43
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