Brugada syndrome in childhood: a potential fatal arrhythmia not always recognised by paediatricians. A case report and review of the literature

Détails

ID Serval
serval:BIB_75CEFDBF1837
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Titre
Brugada syndrome in childhood: a potential fatal arrhythmia not always recognised by paediatricians. A case report and review of the literature
Périodique
European Journal of Pediatrics
Auteur(s)
Mivelaz  Y., Di Bernardo  S., Pruvot  E., Meijboom  E. J., Sekarski  N.
ISSN
0340-6199 (Print)
Statut éditorial
Publié
Date de publication
08/2006
Volume
165
Numéro
8
Pages
507-11
Notes
Case Reports
Journal Article
Review --- Old month value: Aug
Résumé
We report on a youngster followed by his paediatrician from birth until 14 years of age for premature beats, most likely of ventricular origin. The sudden death of his sister provoked a re-assessment of his electrocardiograms (ECG), resulting in the diagnosis of Brugada syndrome and the subsequent implantation of a cardioverter defibrillator. This syndrome is a well known entity in adult cardiology, first described by Brugada and Brugada in 1992. It is considered to be the second most common cause of death in young adults after road traffic accidents. In children, however, the Brugada syndrome is not well known and we believe to be certainly underdiagnosed.
Mots-clé
Adolescent Adult Ajmaline/diagnostic use Brugada Syndrome/*diagnosis/genetics/surgery Death, Sudden/etiology Defibrillators, Implantable Electrocardiography Female Humans Male Siblings Sodium Channel Blockers/diagnostic use Tachycardia, Ventricular/diagnosis/etiology
Pubmed
Web of science
Création de la notice
25/01/2008 11:28
Dernière modification de la notice
03/03/2018 18:24
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