The majority of vestibular schwannomas have a stable evolution or a progression of size. Some publications report cases of spontaneous involution. We report here the clinical and radiological characteristics of this type of tumor observed in 14 patients showing a spontaneous tumor involution of their vestibular schwannoma. The results showed an incidence of 8 % with an average tumor regression of 50 %. Functionally, a hearing loss was found in all patients, without correlation with the duration of the observational follow-up. There are spontaneously involutive vestibular schwannomas, but tumor regression does not prevent the deterioration of hearing. Patients should be considered as a subset of those receiving observational management.