Pneumopathie interstitielle granulomato-lymphocytaire dans l'immunodéficience commune variable [Granulomatous lymphocytic interstitial lung disease in common variable immunodeficiency].

Détails

ID Serval
serval:BIB_6BC47993F101
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Synthèse (review): revue aussi complète que possible des connaissances sur un sujet, rédigée à partir de l'analyse exhaustive des travaux publiés.
Collection
Publications
Titre
Pneumopathie interstitielle granulomato-lymphocytaire dans l'immunodéficience commune variable [Granulomatous lymphocytic interstitial lung disease in common variable immunodeficiency].
Périodique
Revue Médicale Suisse
Auteur(s)
Bianchi M.P., Letovanec I., Spertini F., Nicod L.P., Lazor R.
ISSN
1660-9379 (Print)
ISSN-L
1660-9379
Statut éditorial
Publié
Date de publication
2013
Volume
9
Numéro
407
Pages
2175-2180
Langue
français
Notes
Publication types: English Abstract ; Journal Article Publication Status: ppublish
Résumé
Common variable immunodeficiency (CVID) is the most frequent primary immune deficiency. Recurrent infections are classical consequences of CVID, but their impact has been largely reduced by immunoglobulin replacement. CVID is also associated with various inflammatory and autoimmune manifestations resulting from abnormal cellular immunity. The lungs are especially affected by a recently described entity called granulomatous lymphocytic interstitial lung disease (GLILD). GLILD currently constitutes an important cause of morbidity and mortality in these patients. It is distinct from bronchiectasis secondary to recurrent infections, and presents similarities but also striking differences with sarcoidosis.
Mots-clé
Bronchiectasis/diagnosis, Bronchiectasis/physiopathology, Common Variable Immunodeficiency/diagnosis, Common Variable Immunodeficiency/physiopathology, Granuloma/diagnosis, Granuloma/pathology, Humans, Immunoglobulins/administration & dosage, Lung Diseases, Interstitial/diagnosis, Lung Diseases, Interstitial/physiopathology, Prognosis, Recurrence, Sarcoidosis/diagnosis, Sarcoidosis/physiopathology
Pubmed
Création de la notice
31/03/2014 17:15
Dernière modification de la notice
20/08/2019 15:25
Données d'usage