Article: article from journal or magazin.
Review (review): journal as complete as possible of one specific subject, written based on exhaustive analyses from published work.
Pneumopathie interstitielle granulomato-lymphocytaire dans l'immunodéficience commune variable [Granulomatous lymphocytic interstitial lung disease in common variable immunodeficiency].
Revue Médicale Suisse
Publication types: English Abstract ; Journal Article Publication Status: ppublish
Common variable immunodeficiency (CVID) is the most frequent primary immune deficiency. Recurrent infections are classical consequences of CVID, but their impact has been largely reduced by immunoglobulin replacement. CVID is also associated with various inflammatory and autoimmune manifestations resulting from abnormal cellular immunity. The lungs are especially affected by a recently described entity called granulomatous lymphocytic interstitial lung disease (GLILD). GLILD currently constitutes an important cause of morbidity and mortality in these patients. It is distinct from bronchiectasis secondary to recurrent infections, and presents similarities but also striking differences with sarcoidosis.
Bronchiectasis/diagnosis, Bronchiectasis/physiopathology, Common Variable Immunodeficiency/diagnosis, Common Variable Immunodeficiency/physiopathology, Granuloma/diagnosis, Granuloma/pathology, Humans, Immunoglobulins/administration & dosage, Lung Diseases, Interstitial/diagnosis, Lung Diseases, Interstitial/physiopathology, Prognosis, Recurrence, Sarcoidosis/diagnosis, Sarcoidosis/physiopathology
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