Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkappaB alpha/NF-kappaB pathway in limb-girdle muscular dystrophy type 2A

Détails

ID Serval
serval:BIB_07948DFE01C9
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Institution
Titre
Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkappaB alpha/NF-kappaB pathway in limb-girdle muscular dystrophy type 2A
Périodique
Nature Medicine
Auteur⸱e⸱s
Baghdiguian  S., Martin  M., Richard  I., Pons  F., Astier  C., Bourg  N., Hay  R. T., Chemaly  R., Halaby  G., Loiselet  J., Anderson  L. V., Lopez de Munain  A., Fardeau  M., Mangeat  P., Beckmann  J. S., Lefranc  G.
ISSN
1078-8956 (Print)
Statut éditorial
Publié
Date de publication
05/1999
Volume
5
Numéro
5
Pages
503-11
Notes
Journal Article
Research Support, Non-U.S. Gov't --- Old month value: May
Mots-clé
Adolescent Adult *Apoptosis Biological Transport Calpain/*deficiency/metabolism Cell Compartmentation Cell Nucleus/*pathology Child DNA-Binding Proteins/genetics/*metabolism Female Fetus Fluorescent Antibody Technique Humans *I-kappa B Proteins Male Microscopy, Confocal Muscle, Skeletal/metabolism/pathology Muscular Dystrophies/classification/enzymology/*metabolism/pathology NF-kappa B/antagonists & inhibitors/*metabolism Recombinant Proteins/metabolism
Pubmed
Web of science
Création de la notice
25/01/2008 17:17
Dernière modification de la notice
20/08/2019 13:29
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