Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkappaB alpha/NF-kappaB pathway in limb-girdle muscular dystrophy type 2A
Détails
ID Serval
serval:BIB_07948DFE01C9
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Institution
Titre
Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkappaB alpha/NF-kappaB pathway in limb-girdle muscular dystrophy type 2A
Périodique
Nature Medicine
ISSN
1078-8956 (Print)
Statut éditorial
Publié
Date de publication
05/1999
Volume
5
Numéro
5
Pages
503-11
Notes
Journal Article
Research Support, Non-U.S. Gov't --- Old month value: May
Research Support, Non-U.S. Gov't --- Old month value: May
Mots-clé
Adolescent
Adult
*Apoptosis
Biological Transport
Calpain/*deficiency/metabolism
Cell Compartmentation
Cell Nucleus/*pathology
Child
DNA-Binding Proteins/genetics/*metabolism
Female
Fetus
Fluorescent Antibody Technique
Humans
*I-kappa B Proteins
Male
Microscopy, Confocal
Muscle, Skeletal/metabolism/pathology
Muscular Dystrophies/classification/enzymology/*metabolism/pathology
NF-kappa B/antagonists & inhibitors/*metabolism
Recombinant Proteins/metabolism
DOI
Pubmed
Web of science
Création de la notice
25/01/2008 17:17
Dernière modification de la notice
20/08/2019 13:29