Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkappaB alpha/NF-kappaB pathway in limb-girdle muscular dystrophy type 2A

Details

Serval ID
serval:BIB_07948DFE01C9
Type
Article: article from journal or magazin.
Collection
Publications
Institution
Title
Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkappaB alpha/NF-kappaB pathway in limb-girdle muscular dystrophy type 2A
Journal
Nature Medicine
Author(s)
Baghdiguian  S., Martin  M., Richard  I., Pons  F., Astier  C., Bourg  N., Hay  R. T., Chemaly  R., Halaby  G., Loiselet  J., Anderson  L. V., Lopez de Munain  A., Fardeau  M., Mangeat  P., Beckmann  J. S., Lefranc  G.
ISSN
1078-8956 (Print)
Publication state
Published
Issued date
05/1999
Volume
5
Number
5
Pages
503-11
Notes
Journal Article
Research Support, Non-U.S. Gov't --- Old month value: May
Keywords
Adolescent Adult *Apoptosis Biological Transport Calpain/*deficiency/metabolism Cell Compartmentation Cell Nucleus/*pathology Child DNA-Binding Proteins/genetics/*metabolism Female Fetus Fluorescent Antibody Technique Humans *I-kappa B Proteins Male Microscopy, Confocal Muscle, Skeletal/metabolism/pathology Muscular Dystrophies/classification/enzymology/*metabolism/pathology NF-kappa B/antagonists & inhibitors/*metabolism Recombinant Proteins/metabolism
Pubmed
Web of science
Create date
25/01/2008 17:17
Last modification date
20/08/2019 13:29
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