Atteintes extrarénales de la polykystose rénale: signes cliniques,dépistage et prise en charge [Extra-renal manifestations of the autosomal dominant polycystic kidney disease]

Détails

ID Serval
serval:BIB_B33E3BAED51C
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Titre
Atteintes extrarénales de la polykystose rénale: signes cliniques,dépistage et prise en charge [Extra-renal manifestations of the autosomal dominant polycystic kidney disease]
Périodique
Revue medicale suisse
Auteur(s)
Butscher A., Phan O., Bonny O.
ISSN
1660-9379 (Print)
ISSN-L
1660-9379
Statut éditorial
Publié
Date de publication
22/02/2017
Peer-reviewed
Oui
Volume
13
Numéro
551
Pages
450-456
Langue
français
Notes
Publication types: Journal Article
Publication Status: ppublish
Résumé
Extra-renal complications of autosomal dominant polycystic kidney disease (ADPKD) are often unrecognized. Liver cysts are usually benign, but may cause chronic pain, may interfere with nutrition and may necessitate partial liver resection or even liver transplant. Somatostatin analogs may be an alternative therapy. Cerebral aneurisms are rare, but devastating. They must be investigated in case of positive familial history. Cardiac valvulopathies will be searched for by echocardiography. Abdominal wall herniae are often identified during the physical exam in ADPKD patients. ADPKD patients may present with higher incidence of diverticulitis. Cysts of the seminal vesicle are frequent but are usually asymptomatic. Recognizing extra-renal complications helps improving the overall survival of ADPKD patients.
Mots-clé
Cysts/etiology, Heart Diseases/etiology, Humans, Liver Diseases/etiology, Polycystic Kidney, Autosomal Dominant/complications, Vascular Diseases/etiology
Pubmed
Création de la notice
10/08/2017 15:53
Dernière modification de la notice
12/05/2018 11:47
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