An unusual cause of high anion gap metabolic acidosis: pyroglutamic acidemia. A case report.

Details

Serval ID
serval:BIB_93975F022230
Type
Inproceedings: an article in a conference proceedings.
Publication sub-type
Abstract (Abstract): shot summary in a article that contain essentials elements presented during a scientific conference, lecture or from a poster.
Collection
Publications
Institution
Title
An unusual cause of high anion gap metabolic acidosis: pyroglutamic acidemia. A case report.
Title of the conference
83e assemblée annuelle 2015 de la Société Suisse de Médecine Interne Générale (SSMI)
Author(s)
Gachoud D., Metrailler P., Martiz Aguilar A., Vollenweider P.
Address
Publication types: Case Reports ; Journal Article Publication Status: ppublish 83e assemblée annuelle 2015 de la Société Suisse de Médecine Interne Générale (SSMI), in
Publication types: Case Reports ; Journal Article Publication Status: ppublish
83e assemblée annuelle 2015 de la Société Suisse de Médecine Interne Générale (SSMI), in Praxis 2015; 104 : Suppl 1, p.86
Gachoud D.
Metrailler P.
Martiz Aguilar A.
Vollenweider P.
ISBN
1536-3686 (Electronic)
ISSN-L
1075-2765
Publication state
Published
Issued date
2015
Volume
104
Series
Praxis
Pages
86
Language
english
Abstract
Pyroglutamic acidemia is an uncommon metabolic disorder, which is usually diagnosed at early ages. The mechanism of action is thought to be glutathione depletion, and its clinical manifestations consist of hemolytic anemia, mental retardation, ataxia, and chronic metabolic acidosis. However, an acquired form has been described in adult patients, who usually present with confusion, respiratory distress, and high anion gap metabolic acidosis (HAGMA). It is also associated with many conditions, including chronic acetaminophen consumption. A 68-year-old white male, with chronic acetaminophen use presented to our service on multiple occasions with severe HAGMA. The patient was admitted to the intensive care unit and required mechanical ventilation and aggressive supportive measures. After ruling out the most frequent etiologies for his acid-base disorder and considering the long history of Tylenol ingestion, his 5-oxiproline (pyroglutamic acid) levels were sent to diagnose pyroglutamic acidemia. Clinicians need to be aware of this cause for metabolic acidosis since it might be a more common metabolic disturbance in compromised patients than would be expected. Subjects with HAGMA that cannot be explained by common causes should be tested for the presence of 5-oxoproline. Discontinuation of the offending drug is therapeutic.
Keywords
Acetaminophen/administration & dosage, Acidosis/diagnosis, Acidosis/epidemiology, Acute Kidney Injury/epidemiology, Aged, Analgesics, Non-Narcotic/administration & dosage, Humans, Male, Pyrrolidonecarboxylic Acid/blood
Create date
26/01/2016 12:00
Last modification date
20/08/2019 15:56
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