Significance of lung anomalies in fetuses affected by tetralogy of Fallot with absent pulmonary valve syndrome.

Détails

ID Serval
serval:BIB_F66AE728936E
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Institution
Titre
Significance of lung anomalies in fetuses affected by tetralogy of Fallot with absent pulmonary valve syndrome.
Périodique
Cardiology in the young
Auteur(s)
Tenisch E., Raboisson M.J., Rypens F., Déry J., Grignon A., Lapierre C.
ISSN
1467-1107 (Electronic)
ISSN-L
1047-9511
Statut éditorial
Publié
Date de publication
11/2017
Peer-reviewed
Oui
Volume
27
Numéro
9
Pages
1740-1747
Langue
anglais
Notes
Publication types: Journal Article
Publication Status: ppublish
Résumé
Tetralogy of Fallot with absent pulmonary valve syndrome is a rare form of tetralogy of Fallot with dilatation of large pulmonary arteries. Prognosis is related to the severity of the cardiac malformation and to bronchial tree compression by dilated pulmonary arteries. This study analyses the prenatal echographic lung appearance in fetuses with tetralogy of Fallot with absent pulmonary valve and discusses its significance.
We carried out a retrospective review of fetal and postnatal files of nine fetuses diagnosed with tetralogy of Fallot with absent pulmonary valve syndrome in our institution. Correlations of prenatal ultrasound and cardiac imaging findings were obtained with outcome.
Abnormal heterogeneous fetal lung echogenicity was detected in eight cases out of nine, always associated with significant lobar arterial dilatation. This aspect was well correlated with postnatal imaging and outcome in the four neonatal cases. The only fetus with normal lung echogenicity also had lower degree of pulmonary artery dilatation in the series.
This study demonstrates that a heterogeneous ultrasound appearance of the fetal lungs can be detected in utero in the most severe cases. This aspect suggests an already significant compression of the fetal bronchial tree by the dilated arteries that may have prognostic implications.

Mots-clé
Prenatal diagnosis, absence of pulmonary valve, fetal lung anomaly, fetal ultrasound, tetralogy of Fallot
Pubmed
Web of science
Création de la notice
31/07/2017 14:05
Dernière modification de la notice
20/08/2019 17:22
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