Dilatation idiopathique de l'oreillette droite simulant une maladie d'Ebstein. A propos d'un cas decouvert in utero. [Idiopathic dilatation of the right atrium simulating Ebstein's anomaly. Apropos of a case diagnosed in utero]

Détails

ID Serval
serval:BIB_F51112117F6B
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Institution
Titre
Dilatation idiopathique de l'oreillette droite simulant une maladie d'Ebstein. A propos d'un cas decouvert in utero. [Idiopathic dilatation of the right atrium simulating Ebstein's anomaly. Apropos of a case diagnosed in utero]
Périodique
Archives des Maladies du Coeur et des Vaisseaux
Auteur⸱e⸱s
Reinhardt-Owlya  L., Sekarski  N., Hurni  M., Laurini  R., Payot  M.
ISSN
0003-9683 (Print)
Statut éditorial
Publié
Date de publication
05/1998
Volume
91
Numéro
5
Pages
645-9
Notes
Case Reports
English Abstract
Journal Article --- Old month value: May
Résumé
In October 1992, severe dilatation of the right atrium was detected in a 35 week foetus. The septal leaflet of the tricuspid valve seemed to be displaced distally causing massive tricuspid regurgitation. The diagnosis of Ebstein's anomaly was made and confirmed after birth. Refractory right heart failure occurred at the age of 10 months and the little girl was operated. At surgery, the right atrium was very dilated; the tricuspid valve was normally positioned and was normally constituted. The right atrial wall, partially resected, contained few muscular fibres and showed patchy fibroelastosis. Four years after surgery, the child remains asymptomatic. Dilatation of the right atrium and the tricuspid annulus caused pseudo-displacement of the septal leaflet of the tricuspid valve. This, combined with the importance of tricuspid regurgitation, led to the erroneous diagnosis of Ebstein's anomaly. It is important to differentiate idiopathic right atrial dilatation from Ebstein's anomaly because surgery is much more difficult in the latter case.
Mots-clé
Cardiomyopathy, Dilated/*ultrasonography Diagnosis, Differential Ebstein's Anomaly/*ultrasonography Echocardiography Female Heart Atria/*abnormalities/ultrasonography Humans Pregnancy Ultrasonography, Prenatal
Pubmed
Web of science
Création de la notice
28/01/2008 9:24
Dernière modification de la notice
20/08/2019 16:21
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