Therapeutic strategies in children with an isolated unilaterally absent proximal pulmonary artery.

Détails

ID Serval
serval:BIB_E59E01D07A58
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Titre
Therapeutic strategies in children with an isolated unilaterally absent proximal pulmonary artery.
Périodique
Pediatric cardiology
Auteur⸱e⸱s
Krammoh E.K., Bigras J.L., Prsa M., Lapierre C., Miró J., Dahdah N.S.
ISSN
1432-1971 (Electronic)
ISSN-L
0172-0643
Statut éditorial
Publié
Date de publication
07/2010
Peer-reviewed
Oui
Volume
31
Numéro
5
Pages
607-610
Langue
anglais
Notes
Publication types: Case Reports ; Journal Article
Publication Status: ppublish
Résumé
Therapeutic strategies for isolated unilateral absence of a proximal pulmonary artery remain unclear. The natural history of the disease, or thrombosis of primary surgical anastomosis, leads to exclusion of the affected lung with increased risk of intrapulmonary bleeding, impaired quality of life, and shortened life expectancy. We herein describe our two-stage approach in a small series of patients starting with interventional catheterization followed by surgical anastomosis. Other medical interventions, such as anticoagulation and pulmonary vasodilatation, are key factors to successfully restore pulmonary circulation in this rare defect.
Mots-clé
Anastomosis, Surgical, Anticoagulants/therapeutic use, Blood Vessel Prosthesis Implantation, Cardiac Catheterization, Combined Modality Therapy, Echocardiography, Female, Heart Defects, Congenital/diagnosis, Heart Defects, Congenital/drug therapy, Heart Defects, Congenital/surgery, Humans, Infant, Infant, Newborn, Life Expectancy, Male, Pulmonary Artery/abnormalities, Quality of Life, Vasodilator Agents
Pubmed
Web of science
Création de la notice
10/11/2021 9:56
Dernière modification de la notice
13/04/2024 7:06
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