Inherited disorders of the IL-12-IFN-gamma axis in patients with disseminated BCG infection.
Détails
ID Serval
serval:BIB_E55A99E64269
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Institution
Titre
Inherited disorders of the IL-12-IFN-gamma axis in patients with disseminated BCG infection.
Périodique
European journal of pediatrics
ISSN
0340-6199 (Print)
ISSN-L
0340-6199
Statut éditorial
Publié
Date de publication
12/2005
Peer-reviewed
Oui
Volume
164
Numéro
12
Pages
753-757
Langue
anglais
Notes
Publication types: Case Reports ; Journal Article
Publication Status: ppublish
Publication Status: ppublish
Résumé
Disseminated BCG infection is a rare complication of vaccination that occurs in patients with impaired immunity. In recent years, a series of inherited disorders of the IL-12-IFN-gamma axis have been described that predispose affected individuals to disseminated disease caused by BCG, environmental Mycobacteria, and non-typhoidal Salmonella. The routine immunological work-up of these patients is normal and the diagnosis requires specific investigation of the IL-12-IFN-gamma circuit. We report here the first two such patients originating from and living in Iran. The first child is two years old and suffers from complete IFN-gamma receptor 2 deficiency and disseminated BCG infection. He is currently in clinical remission thanks to prolonged multiple antibiotic therapy. The other, a 28-year-old adult, suffers from IL-12p40 deficiency and presented with disseminated BCG infection followed by recurrent episodes of systemic salmonellosis. He is now doing well. A third patient of Iranian descent, living in North America, was reported elsewhere to suffer from IL-12Rbeta1 deficiency. These three patients thus indicate that various inherited defects of the IL-12-IFN-gamma circuit can be found in Iranian people. In conclusion we recommend to consider the disorders of the IL-12-IFN-gamma circuit in all patients with severe BCG infection, disseminated environmental mycobacterial disease, or systemic non-typhoidal salmonellosis, regardless of their ethnic origin and country of residence.
Mots-clé
Adult, BCG Vaccine/adverse effects, Child, Preschool, Genetic Predisposition to Disease, Humans, Interferon-gamma/genetics, Interleukin-12/genetics, Interleukin-12 Subunit p40, Iran, Male, Mycobacterium bovis, Protein Subunits/genetics, Receptors, Interferon/genetics, Salmonella Infections/genetics, Salmonella Infections/immunology, Tuberculosis/genetics, Tuberculosis/immunology, Tuberculosis/microbiology
Pubmed
Web of science
Création de la notice
04/02/2021 19:04
Dernière modification de la notice
07/07/2021 5:37