Asplénie congénitale (syndrome d'Ivemark) révélée par une thrombose veineuse mésentérique chez un malade de 77 ans [Congenital asplenia (Ivemark syndrome) revealed by mesenteric vein thrombosis in a 77 year old patient].

Détails

ID Serval
serval:BIB_DB3369C9A154
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Titre
Asplénie congénitale (syndrome d'Ivemark) révélée par une thrombose veineuse mésentérique chez un malade de 77 ans [Congenital asplenia (Ivemark syndrome) revealed by mesenteric vein thrombosis in a 77 year old patient].
Périodique
Gastroentérologie Clinique et Biologique
Auteur(s)
Gonzalez M., Collaud S., Gervaz P., Morel P.
ISSN
0399-8320 (Print)
ISSN-L
0399-8320
Statut éditorial
Publié
Date de publication
2007
Volume
31
Numéro
10
Pages
860-862
Langue
français
Notes
Publication types: Case Reports ; English Abstract ; Journal Article
Publication Status: ppublish
Résumé
Congenital asplenia (Ivemark syndrome) is usually associated with major cardiac malformations, which determine the clinical presentation and often result in death before 6 months of age. We report the unusual case of a 77 year-old patient with a congenital asplenia that was incidentally detected during a laparotomy for mesenteric vein thrombosis. The other abnormal findings in the abdomen were a para-esophageal hiatal hernia and left kidney hypotrophy. A segmental resection of the mid-jejunum was performed, with uneventful recovery. A thoraco-abdominal CT scan failed to reveal any associated vascular malformations in the retroperitoneum or the thorax. This case suggests that, in some instances, congenital asplenia, when isolated, may remain asymptomatic and be compatible with a long, and functionally normal life.
Mots-clé
Aged, Humans, Incidental Findings, Kidney/abnormalities, Male, Mesenteric Vascular Occlusion/surgery, Mesenteric Veins/surgery, Spleen/abnormalities, Venous Thrombosis/surgery
Pubmed
Création de la notice
28/09/2015 14:45
Dernière modification de la notice
20/08/2019 16:00
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