Idiopathic pulmonary fibrosis in a Swiss interstitial lung disease reference centre.

Détails

ID Serval
serval:BIB_CA47FF406289
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Titre
Idiopathic pulmonary fibrosis in a Swiss interstitial lung disease reference centre.
Périodique
Swiss medical weekly
Auteur⸱e⸱s
Guler S., Zumstein P., Berezowska S., Pöllinger A., Geiser T., Funke-Chambour M.
ISSN
1424-3997 (Electronic)
ISSN-L
0036-7672
Statut éditorial
Publié
Date de publication
2018
Peer-reviewed
Oui
Volume
148
Pages
w14577
Langue
anglais
Notes
Publication types: Journal Article ; Observational Study
Publication Status: epublish
Résumé
Idiopathic pulmonary fibrosis (IPF) differs substantially from other idiopathic interstitial pneumonias regarding disease trajectory and the appropriate management strategies, making meticulous diagnosis essential. However, patient characteristics and clinical practice vary between clinical trials, and real life and registries provide the opportunity to critically analyse current clinical practices in order to ultimately improve patient care.
We aimed to identify characteristics of our baseline IPF cohort at initiation of a web-based registry for patients with idiopathic interstitial pneumonia. Baseline and 6-month follow-up data from all consecutive IPF patients consulting at our centre over 2 years were analysed.
Forty IPF patients were included for baseline and 23 for longitudinal analysis. Besides many similarities to other IPF populations, our cohort included considerably fewer women. Forced vital capacity impairment in our cohort was more severe and mortality prediction poorer than in clinical trials, which emphasises the importance to confirm the applicability of clinical trial results with data from real life settings.
Registries for rare diseases such as IPF are a valuable resource for studying the course of the disease under current compliance with diagnostic and treatment guidelines and to appreciate local epidemiological particularities.
Mots-clé
Aged, Female, Humans, Idiopathic Pulmonary Fibrosis/diagnosis, Longitudinal Studies, Male, Registries, Retrospective Studies, Sex Factors, Switzerland
Pubmed
Web of science
Open Access
Oui
Création de la notice
29/06/2020 10:35
Dernière modification de la notice
30/06/2020 6:26
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