Intra-abdominal desmoplastic small round cell tumors: CT findings and clinicopathological correlations in 13 cases

Détails

ID Serval
serval:BIB_B330B999D90E
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Titre
Intra-abdominal desmoplastic small round cell tumors: CT findings and clinicopathological correlations in 13 cases
Périodique
Eur J Radiol
Auteur(s)
Chouli M., Viala J., Dromain C., Fizazi K., Duvillard P., Vanel D.
ISSN-L
0720-048X (Print)0720-048X (Linking)
Statut éditorial
Publié
Date de publication
2005
Peer-reviewed
Oui
Volume
54
Numéro
3
Pages
438-42
Langue
anglais
Notes
Chouli, MalikViala, JulietteDromain, ClarisseFizazi, KarimDuvillard, PierreVanel, DanielengIreland2005/05/19 09:00Eur J Radiol. 2005 Jun;54(3):438-42.
Résumé
PURPOSE: We report computed tomography (CT) findings in 13 patients with a primary abdominal desmoplastic small round cell tumor. MATERIALS AND METHODS: 13 cases (12 men, 1 woman, mean age=24.8 years) were found in our hospital database between 1991 and 2003. Clinical, CT and histopathological features were studied retrospectively. RESULTS: Peritoneal involvement was the most common feature. In 10 cases, several lobulated peritoneal soft tissue masses (with a mean of four masses per patient) were seen. Two patients had diffused irregular peritoneal carcinomatosis without any distinct peritoneal masses. One patient had a solitary mass in the pelvic space. The main sites of peritoneal involvement were the pelvic space (n=7), omentum (n=5), retroperitoneal space (n=4), small bowel mesentery (n=3), paracolic gutter (n=2 on the right and n=1 on the left), transverse colon mesentery (n=1), peri-splenic space (n=1), peri-hepatic space (n=1). The soft tissue masses were often bulky (mean 6cm, range 1-28cm), lobulated and heterogeneous with hypodense areas (in 73% of cases). In six cases, moderate ascites was seen. In one case of pelvic involvement, unilateral hydronephrosis was seen. Adenopathies were present in seven cases at the time of the diagnosis (at intraperitoneal, retroperitoneal and pelvic sites in six patients and in the groin in one patient). Five patients had liver metastases (four lesions per case excepted one patient with 30 metastases). Associated thoracic metastases were seen in three patients. The diagnosis was confirmed with four CT-guided percutaneous biopsies. CONCLUSION: Although CT features are nonspecific, the diagnosis of desmoplastic small round cell tumor may be suspected in young men with multiple bulky heterogeneous peritoneal soft tissue masses. Imaging is useful for staging and also to guide biopsies.
Mots-clé
Abdominal Neoplasms/pathology/*radiography, Adolescent, Adult, Child, Diagnosis, Differential, Female, Humans, Male, Radiography, Abdominal, Retrospective Studies, Soft Tissue Neoplasms/pathology/*radiography, Tomography, X-Ray Computed/*methods
Création de la notice
16/09/2016 10:13
Dernière modification de la notice
20/08/2019 15:21
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