Costal exostosis at risk of hepatic injury in a 10-year-old girl
Détails
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Accès restreint UNIL
Etat: Public
Version: de l'auteur⸱e
Licence: CC BY-NC-ND 4.0
ID Serval
serval:BIB_ACAE26D05135
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Institution
Titre
Costal exostosis at risk of hepatic injury in a 10-year-old girl
Périodique
Journal of Pediatric Surgery Case Reports
ISSN
2213-5766
Statut éditorial
Publié
Date de publication
07/2022
Volume
82
Pages
102291
Langue
anglais
Résumé
Hereditary multiple exostosis (HME) is a rare skeletal genetic disorder with multiple and disseminated osteochondromas. Costal localization is found in 40% of cases. Surgery for asymptomatic lesions remains controversial, but some lesions can be life-threatening. We report the case of a 10-year-old girl with HME, who developed a sharp costal exostosis compressing the hepatic parenchyma, for which a prophylactic resection was decided. The complete excision of the lesion was performed through extraperitoneal approach under video-assisted laparoscopy control, without short-and mid-term complication. To our knowledge, our case is the first in the literature where exostosis threatens the hepatic parenchyma.
Mots-clé
Hereditary multiple exostoses (HME)OsteochondromaHepatic rupturePediatric diseaseExploratory laparoscopy
Web of science
Open Access
Oui
Création de la notice
24/06/2022 17:44
Dernière modification de la notice
21/11/2022 7:44