Respiratory surveillance of patients with Duchenne and Becker muscular dystrophy.
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Accès restreint UNIL
Etat: Public
Version: Final published version
Accès restreint UNIL
Etat: Public
Version: Final published version
ID Serval
serval:BIB_5C20BDBDD61F
Type
Article: article d'un périodique ou d'un magazine.
Collection
Publications
Institution
Titre
Respiratory surveillance of patients with Duchenne and Becker muscular dystrophy.
Périodique
Journal of Pediatric Rehabilitation Medicine
ISSN
1874-5393 (Print)
ISSN-L
1874-5393
Statut éditorial
Publié
Date de publication
2009
Volume
2
Numéro
2
Pages
115-122
Langue
anglais
Notes
Publication types: Journal ArticlePublication Status: ppublish
Résumé
Duchenne muscular dystrophy is is the most common form of the childhood muscular dystrophies. It follows a predictable clinical course marked by progressive skeletal muscle weakness, lost of ambulation before teen-age and death in early adulthood secondary to respiratory or cardiac failure. Becker muscular dystrophy is less common and has a milder clinical course but also results in respiratory and cardiac failure.Altough recent advances in respiratory care and new technologies have improved the outlook many patients already received only a traditional non-interventional approach. The aims of this work are: to analyse the pathophysiology and natural history of respiratory function in these diseases, to descript their clinical manifestations, to present the diagnostics tools and to provide recommendations for an adequated respiratory care in this particular population based on the updated literature referenced.
Pubmed
Création de la notice
29/05/2013 13:30
Dernière modification de la notice
20/08/2019 14:14