Childhood Henoch-Schönlein syndrome--common and uncommon features, complications, Finkelstein-Seidlmayer variant and management.

Détails

ID Serval
serval:BIB_33062139D3FC
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Synthèse (review): revue aussi complète que possible des connaissances sur un sujet, rédigée à partir de l'analyse exhaustive des travaux publiés.
Collection
Publications
Titre
Childhood Henoch-Schönlein syndrome--common and uncommon features, complications, Finkelstein-Seidlmayer variant and management.
Périodique
Therapeutische Umschau. Revue therapeutique
Auteur⸱e⸱s
Bucher B., Fiore E., Bernasconi M., Blumberg D., Garzoni L., Rizzi M., Bianchetti M.G.
ISSN
0040-5930 (Print)
ISSN-L
0040-5930
Statut éditorial
Publié
Date de publication
05/2008
Peer-reviewed
Oui
Volume
65
Numéro
5
Pages
269-277
Langue
allemand
Notes
Publication types: English Abstract ; Journal Article ; Review
Publication Status: ppublish
Résumé
Although Henoch-Schönlein syndrome can occur at any age, it is overwhelmingly a disease of childhood. Indeed, Henoch-Schönlein syndrome is the most common vasculitis that affects children. The clinical features of this vasculitis are well documented, and the diagnosis is generally not difficult. This article briefly reviews both common and uncommon clinical aspects of the condition and information concerning therapy. A further focus of this review is recent information concerning abnormalities of immunoglobulin IgA1 glycosylation and the role of aberrantly glycosylated immunoglobulins in the development of Henoch-Schönlein syndrome. The final focus of the article is acute hemorrhagic edema, a benign vasculitis limited to the skin, which is characterized by circinate, medallion-like purpura, and ecchymoses and occurs in children younger than 4 years of age. The nosologic position of acute hemorrhagic edema, which has also been called Finkelstein-Seidlmayer syndrome, as a variant of Henoch-Schönlein syndrome is the subject of considerable debate, but most authors agree that there are sufficient clinical and prognostic differences to consider it a separate entity.
Mots-clé
Child, Humans, Purpura, Schoenlein-Henoch/classification, Purpura, Schoenlein-Henoch/diagnosis, Purpura, Schoenlein-Henoch/therapy, Syndrome
Pubmed
Création de la notice
08/03/2021 11:03
Dernière modification de la notice
13/03/2021 6:26
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