Presentation pulmonaire inhabituelle d'une histiocytose a cellules de Langerhans systemique.

Détails

ID Serval
serval:BIB_0E7F4F6F35D6
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Titre
Presentation pulmonaire inhabituelle d'une histiocytose a cellules de Langerhans systemique.
Périodique
Revue de Médecine Interne
Auteur(s)
Lega  J. C., Cottin  V., Schuller  A., Lazor  R., Jullien  D., Cordier  J. F.
ISSN
0248-8663
Statut éditorial
Publié
Date de publication
08/2008
Peer-reviewed
Oui
Volume
29
Numéro
8
Pages
669-72
Notes
Case Reports
English Abstract
Journal Article
Résumé
An 80-year-old nonsmoking man was referred to our hospital with bilateral perihilar pulmonary opacities. He had a history of epilepsy, sclerosing cholangitis, cutaneous lesions previously diagnosed as localised Langerhans cell histiocytosis. Symptoms included dry cough and dyspnea. Chest CT showed bilateral perihilar alveolar consolidation with bronchiectasis. Histological examination of a lung biopsy showed typical features of Langerhans cell granulomatosis. Investigations revealed anterior and posterior hypopituitarism. An important improvement occurred with corticosteroid and vinblastine treatment.
Mots-clé
Aged, 80 and over Biopsy Bronchiectasis/*etiology Histiocytosis, Langerhans-Cell/*diagnosis Humans Lung/pathology Male
Pubmed
Web of science
Création de la notice
19/12/2008 12:59
Dernière modification de la notice
20/08/2019 13:35
Données d'usage