Acute infantile encephalopathy predominantly affecting the frontal lobe (AIEF): A European case.

Détails

ID Serval
serval:BIB_0B1AAA41AFCD
Type
Article: article d'un périodique ou d'un magazine.
Sous-type
Etude de cas (case report): rapporte une observation et la commente brièvement.
Collection
Publications
Institution
Titre
Acute infantile encephalopathy predominantly affecting the frontal lobe (AIEF): A European case.
Périodique
European Journal of Paediatric Neurology
Auteur⸱e⸱s
Jequier Gygax M., Deonna T., Maeder P., Mayor-Dubois C., Roulet-Perez E.
ISSN
1532-2130[electronic], 1090-3798[linking]
Statut éditorial
Publié
Date de publication
2011
Volume
15
Numéro
2
Pages
158-162
Langue
anglais
Notes
Publication types: JOURNAL ARTICLE
Résumé
Acute infantile encephalopathy predominantly affecting the frontal lobes (AIEF) has been described as a new entity, based on MRI findings (acute abnormal diffusion-weighted imaging signals in the frontal lobes followed by atrophy) and exclusion of other acute encephalopathies. Patients present with acute onset of fever, status epilepticus, and coma. Different causal mechanisms have been suggested such as localized viral infection, toxic insult due to cytokines, or postictal damage. Only children of Japanese descent have been described. We report the case of a Caucasian girl whose history and MRI findings were similar to the Japanese cases. She had a massive regression with verbal apraxia, while cognitive development was less affected; she initially presented with a cluster of complex partial seizures (and not convulsive status epilepticus), making epileptic or post anoxic-ischemic sequelae highly unlikely. The place of this proposed entity among other recently described acute encephalopathies with abnormal diffusion on MRI is discussed.
Pubmed
Création de la notice
25/01/2011 10:57
Dernière modification de la notice
20/08/2019 12:32
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