Ebstein's anomaly: one and a half ventricular repair.

Details

Ressource 1Download: 12458449.pdf (279.80 [Ko])
State: Public
Version: Final published version
License: Not specified
Serval ID
serval:BIB_CF5F06BB6CE5
Type
Article: article from journal or magazin.
Collection
Publications
Institution
Title
Ebstein's anomaly: one and a half ventricular repair.
Journal
Swiss Medical Weekly
Author(s)
Corno A.F., Chassot P.G., Payot M., Sekarski N., Tozzi P., Von Segesser L.K.
ISSN
1424-7860
Publication state
Published
Issued date
2002
Peer-reviewed
Oui
Volume
132
Number
33-34
Pages
485-488
Language
english
Notes
Publication types: Case Reports ; Journal Article - Publication Status: ppublish
Abstract
Patients with Ebstein's anomaly can present after childhood or adolescence with cyanosis, arrhythmias, severe right ventricular dysfunction and frequently with left ventricular dysfunction secondary to the prolonged cyanosis and to the right ventricular interference. At this point conventional repair is accompanied by elevated mortality and morbidity and poor functional results. We report our experience with three patients (8, 16 and 35 years of age) with Ebstein's anomaly, very dilated right atrium, severe tricuspid valve regurgitation (4/4), bi-directional shunt through an atrial septal defect and reduced left ventricular function (mean ejection fraction = 58%, mean shortening fraction = 25%). All underwent one and a half ventricular repair consisting of closure of the atrial septal defect, tricuspid repair with reduction of the atrialised portion of the right ventricle and end-to-side anastomosis of the superior vena cava to the right pulmonary artery. All patients survived, with a mean follow-up of 33 months. In all there was complete regression of the cyanosis and of the signs of heart failure. Postoperative echocardiography showed reduced degree of tricuspid regurgitation (2/4) and improvement of the left ventricular function (mean ejection fraction = 77%, mean shortening fraction = 40%). In patients with Ebstein's anomaly referred late for surgery with severely compromised right ventricular function or even with reduced biventricular function, the presence of a relatively hypoplastic and/or malfunctioning right ventricular chamber inadequate to sustain the entire systemic venous return but capable of managing part of the systemic venous return, permits a one and a half ventricular repair with good functional results.
Keywords
Adolescent, Adult, Child, Cyanosis, Ebstein Anomaly, Echocardiography, Doppler, Color, Female, Heart Atria, Heart Septum, Humans, Male, Time Factors, Treatment Outcome, Tricuspid Valve Insufficiency, Ventricular Dysfunction, Left, Ventricular Dysfunction, Right
Pubmed
Web of science
Create date
28/01/2008 11:43
Last modification date
04/10/2019 11:31
Usage data