La fibrose rétropéritonéale, une maladie inflammatoire méconnue. Observations cliniques et revue de la littérature [Retroperitoneal fibrosis, an unrecognized inflammatory disease. Clinical observations and review of the literature]

Details

Serval ID
serval:BIB_A5091D789AB6
Type
Article: article from journal or magazin.
Publication sub-type
Case report (case report): feedback on an observation with a short commentary.
Collection
Publications
Institution
Title
La fibrose rétropéritonéale, une maladie inflammatoire méconnue. Observations cliniques et revue de la littérature [Retroperitoneal fibrosis, an unrecognized inflammatory disease. Clinical observations and review of the literature]
Journal
Néphrologie
Author(s)
Meier P., Gilabert C., Burnier M., Blanc E.
ISSN
0250-4960
Publication state
Published
Issued date
2003
Peer-reviewed
Oui
Volume
24
Number
4
Pages
173-80
Language
french
Notes
Publication types: Case Reports ; English Abstract ; Journal Article ; Review - Publication Status: ppublish
Abstract
Retroperitoneal fibrosis (RF) is a rare disease, typically with an insidious clinical course. The peak incidence is seen in patients 40 to 60 years of age and mostly in man. The characteristic finding in this disease is a periaortic fibrous mass that often surrounds the ureters. Although usually regarded as an obstructive uropathy, there has been growing recognition of the condition as a generalized disease. It may have a wide variety of manifestations including mediastinitis, thyroiditis and sclerosing cholangitis. The most common mode of presentation remains abdominal or flank pain with uremia, anemia and a high sedimentation rate. Although ultrasound and renal scintigraphy may contribute to the general evaluation of patients with RF, CT-scanner is the preferred imaging method. The multiplanar imaging capability of magnetic resonance may facilitate assessment of disease extent. The pathogenesis of the disease remains unknown. Steroids and, more recently tamoxifen, appear to be effective in the treatment of the RF. In most instances, RF does not lead to long-term morbidity or affect survival. The three cases of RF reported herein illustrate the varied mode of presentation and the response to the treatment.
Keywords
Aged, Anemia, Aortic Aneurysm, Female, Humans, Inflammation, Male, Middle Aged, Pain, Prednisone, Prognosis, Retroperitoneal Fibrosis, Steroids, Surgical Procedures, Operative, Tomography, X-Ray Computed, Uremia
Pubmed
Web of science
Create date
25/01/2008 12:55
Last modification date
20/08/2019 15:10
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