Recurrence of an undifferentiated pleomorphic pulmonary artery sarcoma 8 years after initial presentation: a case report.

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Version: Final published version
License: CC BY 4.0
Serval ID
serval:BIB_702A5D4D48B8
Type
Article: article from journal or magazin.
Publication sub-type
Case report (case report): feedback on an observation with a short commentary.
Collection
Publications
Institution
Title
Recurrence of an undifferentiated pleomorphic pulmonary artery sarcoma 8 years after initial presentation: a case report.
Journal
Frontiers in cardiovascular medicine
Author(s)
Bourlond B., Maurizi N., Antiochos P., Skalidis I., Auf Der Springe K., Royer C., Monney P., Muller O., Kirsch M.
ISSN
2297-055X (Print)
ISSN-L
2297-055X
Publication state
Published
Issued date
2024
Peer-reviewed
Oui
Volume
11
Pages
1378333
Language
english
Notes
Publication types: Case Reports ; Journal Article
Publication Status: epublish
Abstract
Primary cardiac tumors remain exceptionally rare, characterized by a poor prognosis. Among them, sarcomas originating in the pulmonary arteries constitute the most infrequent subgroup within primary cardiac sarcomas.
This report presents the case of a 76-year-old female experiencing a recurrence of an undifferentiated pleomorphic intracardiac pulmonary artery sarcoma located in the right ventricular outflow tract, manifesting 8 years after initial remission. Successful outcomes were attained through a combination of surgical resection, state-of-the-art radiotherapy, and chemotherapy. This comprehensive approach proved essential for optimizing both survival and quality of life.
The unexpectedly prolonged recurrence-free survival observed in this case underscores the effectiveness of the comprehensive multimodal treatment approach outlined in the existing literature. This highlights the pivotal role of a multidisciplinary strategy in addressing primary cardiac sarcomas, particularly those arising in the pulmonary arteries.
Keywords
cardiac MRI, cardiac sarcoma, cardio-oncology, case report, pulmonary artery sarcoma, sarcoma
Pubmed
Web of science
Open Access
Yes
Create date
12/07/2024 13:15
Last modification date
26/07/2024 7:12
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