Erythrokeratodermia variabilis with erythema gyratum repens-like lesions

Details

Serval ID
serval:BIB_6F05422741F8
Type
Article: article from journal or magazin.
Publication sub-type
Case report (case report): feedback on an observation with a short commentary.
Collection
Publications
Institution
Title
Erythrokeratodermia variabilis with erythema gyratum repens-like lesions
Journal
Pediatric Dermatology
Author(s)
Landau  M., Cohen-Bar-Dayan  M., Hohl  D., Ophir  J., Wolf  C. R., Gat  A., Mevorah  B.
ISSN
0736-8046 (Print)
Publication state
Published
Issued date
08/2002
Volume
19
Number
4
Pages
285-92
Notes
Case Reports
Journal Article --- Old month value: Jul-Aug
Abstract
A large pedigree with erythrokeratodermia variabilis (EKV) and erythema gyratum repens-like lesions is described. Clinical, laboratory, and histologic findings of this family are presented. The differential diagnoses of the following dermatoses with an erythematous and a hyperkeratotic component are discussed: erythrokeratodermia variabilis (Mendes da Costa), progressive symmetric erythrokeratoderma (Gottron), loricrin keratoderma, erythrokeratoderma en cocardes (Degos), Netherton syndrome, keratitis-ichthyosis-deafness (KID) syndrome, erythrokeratolysis hiemalis (Oudtshoorn disease), and nonbullous congenital ichthyosiform erythroderma.
Keywords
Adult Aged Biopsy, Needle Child Erythema/genetics/pathology Female *Genetic Predisposition to Disease Heterozygote Humans Hyperkeratosis, Epidermolytic/*genetics/*pathology Ichthyosiform Erythroderma, Congenital/genetics/pathology Immunohistochemistry Infant Infant, Newborn Israel Male Middle Aged Pedigree Prognosis Sampling Studies Severity of Illness Index Skin Diseases, Genetic/diagnosis
Pubmed
Web of science
Create date
25/01/2008 16:35
Last modification date
20/08/2019 14:28
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