Intestinal pseudoobstruction as a paraneoplastic syndrome in ganglioneuroblastoma.

Details

Serval ID
serval:BIB_6BA02E4ADE52
Type
Article: article from journal or magazin.
Publication sub-type
Case report (case report): feedback on an observation with a short commentary.
Collection
Publications
Title
Intestinal pseudoobstruction as a paraneoplastic syndrome in ganglioneuroblastoma.
Journal
European Journal of Pediatric Surgery
Author(s)
Wildhaber B., Niggli F., Stallmach T., Willi U., Stauffer U.G., Sacher P.
ISSN
0939-7248 (Print)
ISSN-L
0939-7248
Publication state
Published
Issued date
2002
Peer-reviewed
Oui
Volume
12
Number
6
Pages
429-431
Language
english
Notes
Publication types: Case Reports ; Journal Article Publication Status: ppublish
Abstract
Intestinal pseudoobstruction may be part of a paraneoplastic syndrome. We report a teenage girl with ganglioneuroblastoma who presented with severe constipation. The intestinal pseudoobstruction was presumed to be due to inflammation of the myenteric plexus with destruction of the ganglion cells caused by antineuronal nuclear antibodies (ANNA or Anti-Hu).
Keywords
Adolescent, Constipation/etiology, Female, Ganglioneuroblastoma/complications, Ganglioneuroblastoma/pathology, Humans, Intestinal Neoplasms/complications, Intestinal Neoplasms/pathology, Intestinal Pseudo-Obstruction/etiology, Intestinal Pseudo-Obstruction/surgery, Myenteric Plexus/physiopathology, Neoplasm Recurrence, Local, Palliative Care, Paraneoplastic Syndromes/diagnosis
Pubmed
Web of science
Create date
21/02/2015 13:24
Last modification date
20/08/2019 15:25
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