An initial MRI picture of limbic encephalitis in subacute sclerosing panencephalitis.

Details

Serval ID
serval:BIB_65C72A63DE56
Type
Article: article from journal or magazin.
Publication sub-type
Case report (case report): feedback on an observation with a short commentary.
Collection
Publications
Institution
Title
An initial MRI picture of limbic encephalitis in subacute sclerosing panencephalitis.
Journal
European Journal of Paediatric Neurology
Author(s)
Lebon S., Maeder P., Maeder-Ingvar M., Poloni C., Mayor-Dubois C., Roulet-Perez E., Jeannet P.Y.
ISSN
1532-2130 (Electronic)
ISSN-L
1090-3798
Publication state
Published
Issued date
2011
Volume
15
Number
6
Pages
544-546
Language
english
Notes
Publication types: Case Reports ; Journal Article Publication Status: ppublish
Abstract
BACKGROUND: Subacute sclerosing panencephalitis (SSPE) is a rare and severe long-term complication of measles. Hallmarks of this entity include progressive cognitive decline, myoclonia, a generalized periodic pattern on EEG and deep white matter abnormalities on MRI. However, imaging can be normal in early stages.
AIM: We report herein the case of a previously healthy 13-years-old girl with an unusual radiological presentation.
RESULTS: She presented with unilateral myoclonia, cognitive decline with memory impairment and a first brain MRI with swelling of both hippocampi mimicking limbic encephalitis. Measles antibodies were positive in CSF and the EEG showed slow periodic complexes.
CONCLUSION: This unusual radiological presentation has never been described in SSPE. Relationship between virus and limbic system are discussed.
Keywords
Adolescent, Cognition Disorders/etiology, Electroencephalography, Epilepsies, Myoclonic/etiology, Female, Humans, Limbic Encephalitis/complications, Limbic Encephalitis/diagnosis, Magnetic Resonance Imaging, Subacute Sclerosing Panencephalitis/complications, Subacute Sclerosing Panencephalitis/diagnosis
Pubmed
Web of science
Create date
04/07/2011 18:31
Last modification date
20/08/2019 15:21
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