Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan's Syndrome.

Details

Serval ID
serval:BIB_62A38FBA2C61
Type
Article: article from journal or magazin.
Collection
Publications
Institution
Title
Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan's Syndrome.
Journal
Case reports in ophthalmology
Author(s)
Voulgari N., Giacuzzo C., Schalenbourg A., Kymionis G.D.
ISSN
1663-2699 (Print)
ISSN-L
1663-2699
Publication state
Published
Issued date
2019
Peer-reviewed
Oui
Volume
10
Number
3
Pages
344-348
Language
english
Notes
Publication types: Case Reports
Publication Status: epublish
Abstract
We report a case of occult spontaneous ocular perforation presenting as conjunctival chemosis in a patient with Marfan's syndrome (MFS). A 38-year-old female with MFS presented with bilateral conjunctival chemosis since 6 months. Best-corrected visual acuity was 20/20 in both eyes. On slit-lamp examination, a diffuse conjunctival chemosis was observed in both eyes without any signs of ocular hypotony (decreased visual acuity, low intraocular pressure, shallow anterior chamber, pupil distortion, hypotony maculopathy, and chorioretinal folds). Anterior-segment optical coherence tomography revealed a corneoscleral fistula at the left nasal limbus, without any similar finding in the right eye. A scleral patch was performed at the site of the perforation. At 3 month's follow-up, the left chemosis had regressed, with a stable best-corrected visual acuity in both eyes. However, on ultrasound biomicroscopy, another fistula at the right superior limbus was found, and the patient was referred for treatment with a scleral patch. In conclusion, conjunctival chemosis in a patient with MFS should raise the suspicion of an occult spontaneous ocular perforation.
Keywords
Conjunctival chemosis, Marfan's syndrome, Occult ocular perforation
Pubmed
Open Access
Yes
Create date
05/12/2019 23:53
Last modification date
14/12/2019 7:26
Usage data