Intracranial hypotension in a girl with Marfan syndrome: case report and review of the literature.

Details

Serval ID
serval:BIB_622122780B72
Type
Article: article from journal or magazin.
Collection
Publications
Institution
Title
Intracranial hypotension in a girl with Marfan syndrome: case report and review of the literature.
Journal
Child's nervous system
Author(s)
Cheuret E., Edouard T., Mejdoubi M., Acar P., Pienkowski C., Cances C., Lebon S., Tauber M., Chaix Y.
ISSN
0256-7040 (Print)
ISSN-L
0256-7040
Publication state
Published
Issued date
04/2008
Peer-reviewed
Oui
Volume
24
Number
4
Pages
509-513
Language
english
Notes
Publication types: Case Reports ; Journal Article ; Review
Publication Status: ppublish
Abstract
A 14-year-old girl, followed in our department for Marfan syndrome, presented with postural headache for a month. Neurological examination was normal. The diagnosis of intracranial hypotension syndrome was suspected.
Bilateral subdural hematomas were found on brain magnetic resonance imaging (MRI), and spinal MRI showed large lumbosacral arachnoid diverticula; no cerebrospinal fluid leaks could be found. Despite bed rest and hydration for 2 weeks, postural headache remained. Epidural blood patching was also performed. Subsequently, the patient became asymptomatic and could stand up after 1 day. Brain MRI did not find recurrent subdural hematoma after 1 month. Dural ectasia is one of the major criteria of Marfan syndrome, and it is often poorly symptomatic. Intracranial hypotension is a rare complication especially in children, and management is not standardized. In this case report, blood patching was sufficient. Further research into the diagnosis and management of spontaneous intracranial hypotension is required.
Keywords
Adolescent, Brain/pathology, Female, Humans, Intracranial Hypertension/etiology, Magnetic Resonance Imaging, Marfan Syndrome/complications, Marfan Syndrome/pathology, Spinal Cord/pathology
Pubmed
Web of science
Create date
24/01/2020 19:04
Last modification date
25/01/2020 7:26
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