Dix-huit cas de dysplasie fibreuse craniofaciale [Eighteen cases of craniofacial fibrous dysplasia]

Details

Serval ID
serval:BIB_32FE117E257B
Type
Article: article from journal or magazin.
Collection
Publications
Title
Dix-huit cas de dysplasie fibreuse craniofaciale [Eighteen cases of craniofacial fibrous dysplasia]
Journal
Revue de stomatologie et de chirurgie maxillo-faciale
Author(s)
Ziadi S., Trimeche M., Mokni M., Sriha B., Khochtali H., Korbi S.
ISSN
1776-257X (Electronic)
ISSN-L
0035-1768
Publication state
Published
Issued date
12/2009
Peer-reviewed
Oui
Volume
110
Number
6
Pages
318-322
Language
french
Notes
Publication types: English Abstract ; Journal Article
Publication Status: ppublish
Abstract
Fibrous dysplasia or Jaffe Lischtenstein's disease is sporadic and rare bone affection, mainly observed in young adults. It is characterized by a bone maturation disorder that can affect one or several bones. Fibrous dysplasia is relatively rare in the craniofacial region, (only 20% of all locations). The authors analyzed the epidemiological, anatomoclinical and evolutive features of fibrous dysplasia in a Tunisian population.
The authors retrospectively studied 18 cases of craniofacial fibrous dysplasia, diagnosed at the pathology department of the Sousse F. Hached hospital, beween1990 and 2005.
Most craniofacial dysplasia cases were monostotic (94% of cases). One case was polyostotic. The maxilla and the mandible were the most frequent locations (83.3%). The patients' mean age was 28.6 years, ranging from 6 to 30 years. The sex ratio was 3.5 in favor of women. Follow-up ranged from one month to 10 years with an average of 26.4 months. One case of sarcomatous transformation was observed.
The authors noted epidemiological discrepancies compared to what was usually reported, especially concerning the strong female predominance, the frequency of maxillary and mandibular locations and the predominance of monostotic presentations. Larger series are needed to validate these observations.
Keywords
Adolescent, Adult, Age Factors, Cell Transformation, Neoplastic/pathology, Child, Epidemiologic Studies, Facial Bones/pathology, Female, Fibrous Dysplasia, Monostotic/epidemiology, Follow-Up Studies, Humans, Male, Mandibular Diseases/epidemiology, Maxillary Diseases/epidemiology, Osteosarcoma/pathology, Retrospective Studies, Sex Factors, Skull Neoplasms/pathology, Tunisia/epidemiology, Young Adult
Pubmed
Web of science
Create date
17/10/2023 10:06
Last modification date
20/10/2023 7:10
Usage data