Fibromuscular dysplasia (FMD) is a heterogeneous group of nonatherosclerotic, noninflammatory vascular diseases that can be classified into 2 subtypes based on their angiographic appearance: the multifocal type, with its typical string-of-beads pattern, and the unifocal type, presenting as a single focal stenosis.1,2 Because these 2 FMD entities differ substantially with regard to clinical and histopathologic characteristics, it has been suggested that unifocal and multifocal FMDs in fact represent 2 different vascular diseases.3 Recently, however, we observed a patient in whom imaging studies suggest the coexistence of unifocal and multifocal FMD in a single patient.